This study reports on the long-term results of aortic valve balloon dilatation (AVBD) for congenital valvular aortic stenosis in children and young adults. Data from 74 patients (age range: 1-20 years) were analyzed retrospectively. The procedure was successful in 71 patients (96%). The mean (± SD) reduction in peak-to-peak systolic gradient (PSG) was 68.7 ± 13.5%. No patient required immediate surgical intervention. Survival after dilatation was 100% at 12 years. At follow up (mean 5.5 ± 2.9 years; range: 2-12 years), 20% of patients had restenosis and 21% had significant aortic regurgitation (grade ≥3). Reintervention was performed in 14% of patients. Severity of aortic regurgitation and high residual stenosis immediately after AVBD were associated with the late event rates. Actuarial intervention-free rates at five, seven and 12 years were 92.9%, 84.4% and 60%, respectively. AVBD is a useful, albeit palliative, procedure for children and young adults with significant valvular aortic stenosis.